Krebs-Henseleit 1932: 5-step cycle in liver mitochondria + cytoplasm converting NH₃ + CO₂ + aspartate → urea + fumarate. Net stoichiometry: 2 NH₄⁺ + HCO₃⁻ + 3 ATP → urea + 2 ADP + AMP + 4 Pᵢ. Inborn errors (OTC deficiency, citrullinemia)…
Krebs-Henseleit 1932: 5-step cycle in liver mitochondria + cytoplasm converting NH₃ + CO₂ + aspartate → urea + fumarate. Net stoichiometry: 2 NH₄⁺ + HCO₃⁻ + 3 ATP → urea + 2 ADP + AMP + 4 Pᵢ. Inborn errors (OTC deficiency, citrullinemia)…